Variable cMyBP-C expression from cell to cell in a MYBPC3(c.927-2 A>G) hiPSC-CM model recapitulates HCM patient phenotype

Summary

This study presents a validated hiPSC-based model of MYBPC3-associated HCM that captures the variability in protein expression and functional phenotype observed in patient heart tissue. Our findings support the relevance of single-cell transcriptional variability in HCM pathogenesis and highlight the utility of this model for future studies. © 2026. The Author(s).

Authors Ivaskevica K, Kowalski K, Piep B, Teske J, Meissner JD, Kosanke M, Radocaj A, Montag J, Zweigerdt R, Kraft T, Konze SA
Journal Stem cell research & therapy
Publication Date 2026 May 19;17(1)
PubMed 42152135
PubMed Central PMC13185243
DOI 10.1186/s13287-026-05063-9

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