IBCHi001-A

Registration Summary:

A P E C

iDRPLA_8

The cell line is not submitted yet.

(only basic data is shown)

General

iPSC Line
hPSCreg name	IBCHi001-A
Cite as:	IBCHi001-A (RRID:CVCL_XC40)
Alternative name(s)	iDRPLA_8
iPSC line type	Human induced pluripotent stem cell (hiPSC)
Similar iPSC lines	No similar lines found.
Last update	8th February 2019
User feedback	Written by on No feedback available yet. Login to share your feedback, experiences or results with the research community.
Provider
Generator	Institute of Bioorganic Chemistry Polish Academy of Sciences (IBCH)
External iPSC Databases
Cellosaurus	CVCL_XC40
Wikidata	Q94312588
General iPSC Information
Publications	Kozlowska E et al. Generation of human iPS cell line IBCHi001-A from dentatorubral-pallidoluysian atrophy patient's fibroblasts. Stem cell research. 2019 Aug;39:101512. Naphade S et al. Modeling Polyglutamine Expansion Diseases with Induced Pluripotent Stem Cells. Neurotherapeutics : the journal of the American Society for Experimental NeuroTherapeutics. 2019 Oct;16(4):979-998. Ciolak A et al. Generation of human iPS cell line IBCHi002-A from spinocerebellar ataxia type 3/Machado-Joseph disease patient's fibroblasts. Stem cell research. 2020 May;45:101796. Hirose S et al. Application of induced pluripotent stem cells in epilepsy. Molecular and cellular neurosciences. 2020 Oct;108:103535. He L et al. Human stem cell models of polyglutamine diseases: Sources for disease models and cell therapy. Experimental neurology. 2021 Mar;337:113573. Nowak B et al. Atrophin-1 Function and Dysfunction in Dentatorubral-Pallidoluysian Atrophy. Movement disorders : official journal of the Movement Disorder Society. 2023 Apr;38(4):526-536. Nuga Oluwademilade et al. Disrupted Transcriptional Networks in Mammalian Cells Stably Over‐Expressing Pathogenic Atrophin‐1. Journal of Neuroscience Research. 2025-12-00. Satheesh Parvathi et al. Experimental Models of Polyglutamine Disorders. Contemporary Clinical Neuroscience. 2026-00-00.

iPSC Derivation

General